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SDHC germline pathogenic variant

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBIO-SDHC-GERMLINE
TypeBiomarker
Aliases
SDHC germline патогенний варіант
Statusreviewed 2026-05-18 | pending_clinical_signoff
DiseasesNone declared
SourcesSRC-NCCN-BCELL-2025

Biomarker Facts

Biomarker typegene_mutation
Mutation details{"functional_impact": "loss_of_function", "gene": "SDHC", "gene_hugo_id": "HGNC:10683", "variant_type": "missense_or_truncating"}
Related biomarkersNone declared

Notes

SDHC germline — drives hereditary paraganglioma-pheochromocytoma syndrome (PGL3). Predominantly head-and-neck paraganglioma (typically benign, low malignant potential vs SDHB). SDH-deficient GIST + rare RCC. Lower lifetime penetrance than SDHB/SDHD. Annual biochemistry (metanephrines) + whole-body MRI surveillance per NCCN. STUB pending two-Co-Lead signoff.

Used By

No reverse references found in the YAML corpus.