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ROS1 rearrangement in advanced NSCLC: entrectinib (CNS-active) and crizotinib have establ...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-ROS1-FUSION-NSCLC
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-NSCLC
SourcesSRC-CIVIC SRC-ESMO-NSCLC-METASTATIC-2024 SRC-NCCN-NSCLC-2025

Actionability Facts

BiomarkerBIO-ROS1-FUSION
Variantfusion (gene-level, TKI-naive)
DiseaseDIS-NSCLC
ESCAT tierIA
Recommended combinationsrepotrectinib monotherapy (preferred 1L), entrectinib monotherapy (1L, CNS-active), crizotinib monotherapy (1L alternative, less CNS activity)
Evidence summaryROS1 rearrangement in advanced NSCLC: entrectinib (CNS-active) and crizotinib have established 1L approvals. Repotrectinib (TRIDENT-1, Drilon 2024) demonstrated superior PFS and CNS activity 1L — including activity vs G2032R resistance — and is increasingly preferred. Lorlatinib also active off-label.

Notes

ESCAT IA. OncoKB Level 1. ~1-2% NSCLC adenocarcinoma. RNA-NGS preferred for fusion detection; FISH and IHC alternatives.

Used By

No reverse references found in the YAML corpus.