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BRIP1 (FANCJ) germline pathogenic in EOC: established moderate-risk gene (~RR 3-5); inclu...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-BRIP1-GERMLINE-OVARIAN
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-OVARIAN
SourcesSRC-CIVIC SRC-ESMO-OVARIAN-2024 SRC-NCCN-OVARIAN-2025

Actionability Facts

BiomarkerBIO-HRR-PANEL
VariantBRIP1 germline pathogenic
DiseaseDIS-OVARIAN
ESCAT tierIIA
Recommended combinationsniraparib maintenance, olaparib + bevacizumab (HRD-positive), rucaparib (LOH-high)
Evidence summaryBRIP1 (FANCJ) germline pathogenic in EOC: established moderate-risk gene (~RR 3-5); included in HRR panels and HRD-positive PARPi trial subgroups. NCCN includes BRIP1 in PARPi-eligible HRR list. ESCAT IIA / OncoKB Level 3A.

Notes

Cascade testing per NCCN. Modest breast-cancer risk in relatives.

Used By

No reverse references found in the YAML corpus.