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TP53-mut CLL contraindicates chemoimmunotherapy (FCR/BR). BTKi (acalabrutinib, zanubrutin...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-TP53-MUT-CLL
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-CLL
SourcesSRC-CIVIC SRC-ESMO-CLL-2024 SRC-NCCN-BCELL-2025

Actionability Facts

BiomarkerBIO-TP53-MUTATION
Variantany pathogenic mutation OR del(17p)
DiseaseDIS-CLL
ESCAT tierIIIA
Recommended combinationsacalabrutinib monotherapy, zanubrutinib monotherapy, venetoclax + obinutuzumab (CLL14), BTKi + venetoclax (CAPTIVATE / GLOW)
Evidence summaryTP53-mut CLL contraindicates chemoimmunotherapy (FCR/BR). BTKi (acalabrutinib, zanubrutinib, ibrutinib) or BCL2i (venetoclax + obinutuzumab; CLL14) preferred. Some guidelines favor venetoclax-based fixed-duration over continuous BTKi for high-risk; data evolving.

Notes

ESCAT IIIA. Gene-level cell — biallelic vs monoallelic distinction matters in MDS/AML (biallelic = TP53-multihit per IPSS-M / ICC 2022, far worse). Per-hotspot cells provided for the most common variants.

Used By

No reverse references found in the YAML corpus.