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PDGFRA exon 12 mutations in GIST are imatinib-sensitive. Imatinib 400 mg/day is standard...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-PDGFRA-EXON12-GIST
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-GIST
SourcesSRC-CIVIC SRC-IRIS-OBRIEN-2003 SRC-NCCN-MELANOMA-2025

Actionability Facts

BiomarkerBIO-PDGFRA
Variantexon 12 mutation (juxtamembrane domain — V561D most common; rare <2% GIST)
DiseaseDIS-GIST
ESCAT tierIB
Recommended combinationsimatinib 400 mg/day (1L advanced/metastatic)
Evidence summaryPDGFRA exon 12 mutations in GIST are imatinib-sensitive. Imatinib 400 mg/day is standard 1L — response rates comparable to KIT exon 11 and PDGFRA non-D842V exon 18. Rare genotype (<2% of GIST).

Notes

ESCAT IB. OncoKB Level 1. Source-gap as DIS-GIST.

Used By

No reverse references found in the YAML corpus.