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IDH2 R140Q (~5-9% of AML). Enasidenib (IDHIFA, AG221-C-001 Stein et al. Blood 2017) FDA-a...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-IDH2-R140Q-AML
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-AML
SourcesSRC-CIVIC SRC-ELN-AML-2022 SRC-NCCN-AML-2025

Actionability Facts

BiomarkerBIO-IDH-MUTATION
VariantIDH2 R140Q
DiseaseDIS-AML
ESCAT tierIA
Recommended combinationsenasidenib monotherapy, enasidenib + azacitidine (1L unfit, off-label/trial)
Evidence summaryIDH2 R140Q (~5-9% of AML). Enasidenib (IDHIFA, AG221-C-001 Stein et al. Blood 2017) FDA-approved 2017 for R/R IDH2-mut AML. IDHENTIFY (Ph3) confirmed OS benefit late-line. Combos with azacitidine (Ph2) promising 1L unfit.

Notes

ESCAT IA. OncoKB Level 1. Differentiation syndrome AE class effect.

Used By

No reverse references found in the YAML corpus.