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IDH1 R132 mutations (~6-10% of AML). Ivosidenib monotherapy (AGILE, Montesinos et al. NEJ...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-IDH1-R132H-AML
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-AML
SourcesSRC-CIVIC SRC-ELN-AML-2022 SRC-ESMO-AML-2020 SRC-NCCN-AML-2025

Actionability Facts

BiomarkerBIO-IDH-MUTATION
VariantIDH1 R132H
DiseaseDIS-AML
ESCAT tierIA
Recommended combinationsivosidenib monotherapy, ivosidenib + azacitidine (1L unfit), olutasidenib monotherapy, ivosidenib + 7+3 (frontline fit, in trials)
Evidence summaryIDH1 R132 mutations (~6-10% of AML). Ivosidenib monotherapy (AGILE, Montesinos et al. NEJM 2022 — combo with azacitidine; AG120-C-001 — monotherapy in R/R) FDA-approved. Ivosidenib + azacitidine (1L unfit, AGILE) doubles OS vs azacitidine alone.

Notes

ESCAT IA. Differentiation syndrome class AE — prophylactic dexamethasone protocol per ELN. Companion dx: Abbott RealTime IDH1.

Used By

No reverse references found in the YAML corpus.