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FLT3-ITD in B-ALL is rare (~1-3% adult; enriched in MLL/KMT2A- rearranged infant ALL). Gi...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-FLT3-ITD-B-ALL
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-B-ALL
SourcesSRC-CIVIC SRC-NCCN-AML-2025

Actionability Facts

BiomarkerBIO-FLT3-ITD
Variantinternal tandem duplication (rare in B-ALL ~1-3%, MLL-rearranged enriched)
DiseaseDIS-B-ALL
ESCAT tierIIIA
Recommended combinationsclinical trial (FLT3i basket; gilteritinib + chemo)
Evidence summaryFLT3-ITD in B-ALL is rare (~1-3% adult; enriched in MLL/KMT2A- rearranged infant ALL). Gilteritinib and midostaurin have basket activity in FLT3-mutant ALL but no phase-3 evidence. Tumor-agnostic FLT3i actionability is informed by AML data; specific B-ALL trials pending.

Notes

ESCAT IIIA. OncoKB Level 3B. Standard B-ALL therapy (pediatric- inspired chemo / blinatumomab / inotuzumab / CAR-T) applies; FLT3 status does not currently modify treatment.

Used By

No reverse references found in the YAML corpus.