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BRAF V600E in adult-type glioblastoma is rare (~1-3%) but more common in epithelioid GBM...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-BRAF-V600E-GBM
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-GBM
SourcesSRC-CIVIC SRC-EANO-GBM-2024 SRC-NCCN-CNS-2025

Actionability Facts

BiomarkerBIO-BRAF-V600E
VariantV600E
DiseaseDIS-GBM
ESCAT tierIIIA
Recommended combinationsdabrafenib + trametinib (recurrent / progressive after RT + TMZ)
Contraindicated monotherapyvemurafenib monotherapy (limited CNS penetration, paradoxical RAS-RAF activation in BRAF-WT clones)
Evidence summaryBRAF V600E in adult-type glioblastoma is rare (~1-3%) but more common in epithelioid GBM and pediatric high-grade glioma. Dabrafenib + trametinib is tissue-agnostic FDA-approved (2022) for BRAF V600E solid tumors after progression on prior therapy — covers BRAF V600E GBM (Wen et al. ROAR-glioma 2022, ORR 33% in HGG). Vorasidenib does NOT apply here (IDH-mutant only).

Notes

ESCAT IIIA. OncoKB Level 2 (tissue-agnostic). Reflex BRAF V600E testing recommended for epithelioid GBM and pediatric/AYA HGG. Distinct from low-grade pediatric glioma where BRAFi has stronger evidence.

Used By

No reverse references found in the YAML corpus.