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BCR-ABL1 V299L confers resistance to dasatinib and bosutinib but retains sensitivity to n...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-BCR-ABL1-V299L-CML
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-CML
SourcesSRC-CIVIC SRC-ELN-CML-2020 SRC-ELN-CML-2025

Actionability Facts

BiomarkerBIO-BCR-ABL1
VariantV299L
DiseaseDIS-CML
ESCAT tierIB
Recommended combinationsnilotinib monotherapy, ponatinib monotherapy
Contraindicated monotherapydasatinib (resistant), bosutinib (resistant)
Evidence summaryBCR-ABL1 V299L confers resistance to dasatinib and bosutinib but retains sensitivity to nilotinib and ponatinib. Switch to nilotinib is standard salvage; ponatinib reserved for multi-TKI-resistant.

Notes

OncoKB R2. Recurrent dasatinib/bosutinib-resistance mutation; treatment switch driven by ELN mutation-guided algorithm.

Used By

No reverse references found in the YAML corpus.