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TP53 hotspot R282W in higher-risk MDS — dismal prognosis. Biallelic vs monoallelic per IP...

Deterministic view of the source YAML entity. Clinical authority remains with the cited source IDs and reviewer sign-off state.

IDBMA-TP53-R282W-MDS-HR
TypeActionability
Statusreviewed 2026-04-27 | pending_clinical_signoff | actionability review required
DiseasesDIS-MDS-HR
SourcesSRC-CIVIC SRC-ESMO-MDS-2021 SRC-IPSS-M-BERNARD-2022

Actionability Facts

BiomarkerBIO-TP53-MUTATION
VariantR282W
DiseaseDIS-MDS-HR
ESCAT tierIIIB
Recommended combinationsazacitidine + venetoclax, alloSCT consideration, clinical trial
Evidence summaryTP53 hotspot R282W in higher-risk MDS — dismal prognosis. Biallelic vs monoallelic per IPSS-M scoring critical.

Notes

ESCAT IIIB. R282W hotspot — score per IPSS-M biallelic algorithm.

Used By

No reverse references found in the YAML corpus.